Case Report: DARS Mutations Responsible for Hypomyelination With Brain Stem and Spinal Cord Involvement and Leg Spasticity

Objective: Hypomyelination with brain stem and spinal cord involvement and leg spasticity (HBSL) is a rare form of leukodystrophy presenting with varying clinical chevy equinox steering wheel cover and imaging features.We report a case of HBSL to investigate the clinical and radiological characteristics of HBSL resulting from cytoplasmic aspartyl-t

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Multi-Branch Deep Fusion Network-Based Automatic Detection of Weld Defects Using Non-Destructive Ultrasonic Test

This study introduces a deep learning engine designed for the non-destructive automatic detection of defects within weld beads.A 1D waveform ultrasound signal was collected using an A-scan pulser wedding bands in fresno receiver to gather defect signals from inside the weld bead.We established 5,108 training datasets and 500 test datasets for five

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